Clinical Physiology of Circulation

Chief Editor

Leo A. Bockeria, MD, PhD, DSc, Professor, Academician of Russian Academy of Sciences, Director of Bakoulev National Medical Research Center for Cardiovascular Surgery

Heart rhythm disorders with corrected transposition of the great arteries: natural course, diagnosis and treatment

Authors: Khasiev S.G., Samsonov V.B., Mataev V.S.

Company:
Bakoulev National Medical Research Center for Cardiovascular Surgery, Moscow, 121552, Russian Federation

E-mail: Сведения доступны для зарегистрированных пользователей.

DOI: https://doi.org/10.24022/1814-6910-2021-18-1

UDC: 616.12-007-053.1-052-089.168.1-06:616.12-008.318

Link: Clinical Physiology of Blood Circulaiton. 2021; 1 (18): 30-36

Quote as: Khasiev S.G., Samsonov V.B., Mataev V.S. Heart rhythm disorders with corrected transposition of the great arteries: natural course, diagnosis and treatment. Clinical Physiology of Circulation. 2021; 18 (1): 30–6 (in Russ.). DOI: 10.24022/1814-6910-2021-18-1-30-36

Received / Accepted:  07.07.2020 / 03.08.2020

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Abstract

Conduction system and heart rhythm disorders in patients with congenitally corrected transposition of the great arteries (CCTGA), along with heart failure, are the most significant risk factors for death. Treatment methods include both conservative and interventional approaches, with the use of catheter ablation and pacemaker implantation. Until now, there is still no consensus which is better – to implant an epicardial or endocardial system, especially in children. This article presents a short literature review, describing on the features of the anatomy of the conducting system, diagnosis and treatment of heart rhythm and conduction disorders in patients with CCTGA.

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****
  1. Harrison D.A., Connelly M., Harris L., Luk C., Webb G.D., McLaughlin P.R. Sudden cardiac death in the adult with congenital heart disease. Can. J. Cardiol. 1996; 12: 1161–3.
  2. Agarwal A., Samad F., Kalvin L., Bush M., Tajik A.J. A great imitator in adult cardiology practice: congenitally corrected transposition of the great arteries. Cong. Heart Dis. 2017; 12 (2): 143–52. DOI: 10.1111/chd.12453
  3. Baruteau A.-E., Abrams D.J., Yen Ho S., Thambo J.-B., McLeod Ch.J., Shah M.J. Cardiac conduction system in congenitally corrected transposition of the great arteries and its clinical relevance. J. Am. Heart Assoc. 2017; 6 (12): e007759. DOI: 10.1161/JAHA.117. 007759
  4. Kasar T., Ayyildiz P., Tunca Sahin G., Ozturk E., Gokalp S., Haydin S. et al. Rhythm disturbances and treatment strategies in children with congenitally corrected transposition of the great arteries. Congenit. Heart Dis. 2018; 13 (3): 450–7. DOI: 10.1111/chd.12595
  5. Simmons M.A., Rollinson N., Fishberger S., Li Qin, Fahey J., Elder R.W. Modern incidence of complete heart block in patients with L-looped ventricles: does univentricular status matter? Congenit. Heart Dis. 2015; 10 (5): E237–E242. DOI: 10.1111/chd.12279
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  9. Walsh E.P., Cecchin F. Arrhythmias in adult patients with congenital heart disease. Circulation. 2007; 115 (4): 534–45. DOI: 10.1161/CIRCULATIONAHA.105. 592410
  10. Daliento L., Corrado D., Buja G., John N., Nava A., Thiene G. Rhythm and conduction disturbances in isolated, congenitally corrected transposition of the great arteries. Am. J. Cardiol. 1986; 58 (3): 314–8. DOI: 10.1016/0002-9149(86)90069-x
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  16. Lin J.H., Kean A.C., Cordes T.M. The risk of thromboembolic complications in Fontan patients with atrial flutter/fibrillation treated with electrical cardioversion. Pediatr. Cardiol. 2016; 37 (7): 1351–60. DOI: 10.1007/s00246-016-1441-4
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  22. Pujol C., Niesert A.-C., Engelhardt A., Schoen P., Kusmenkov E., Pittrow D. et al. Usefulness of direct oral anticoagulants in adult congenital heart disease. Am. J. Cardiol. 2016; 117 (3): 450–5. DOI: 10.1007/s12012-016-9380-0
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  24. Ergül Ya., Esen O., Özgür S., Güzeltas, A. Catheter ablation of manifest posteroseptal accessory pathway associated with coronary sinus diverticula in a child with congenitally corrected transposition of the great arteries. Anatol. J. Cardiol. 2018; 19 (2): 149–51. DOI: 10.14744/AnatolJCardiol.2017.8108
  25. Chavan Ch., Rao H.B., Badani R.S., Raju P.R., Narasimhan C. Ablation of incessant orthodromic reciprocating tachycardia in a child with congenitally corrected transposition of great arteries and ebsteinoid malformation of left atrioventricular valve. J. Interv. Card. Electrophysiol. 2008; 23 (2): 149–52. DOI: 10.1007/s10840-008-9283-5
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  27. Kleinman M.E., de Caen A.R., Chameides L., Atkins D.L., Berg M.D., Bhanji F. et al. Pediatric basic and advanced life support: 2010 International consensus on cardiopulmonary resuscitation and emergency cardiovascular care science with treatment recommendations. Pediatrics. 2010; 126 (5): e1261–318. DOI: 10.1542/peds.2010-2972A
  28. Kanter R.J., Pfeiffer R., Hu D., Barajas-Martinez Y., Carboni M.P., Antzelevitch C. Brugada-like syndrome in infancy presenting with rapid ventricular tachycardia and intraventricular conduction delay. Circulation. 2012; 125 (1): 14–22. DOI: 10.1161/CIRCULATIONAHA.111.054007
  29. Khairy P., Landzberg M.J., Gatzoulis M.A., Mercier L.-A., Fernandes S.M., Cote J-M. et al. Transvenous pacing leads and systemic thromboemboli in patients with intracardiac shunts: a multicenter study. Circulation. 2006; 113 (20): 2391–7. DOI: 10.1161/CIRCULATIONAHA.106.622076
  30. Takeuchi D., Tomizawa Y. Pacing device therapy in infants and children: a review. J. Artif. Organs. 2013; 16 (1): 23–33. DOI: 10.1007/s10047-012-0668-y
  31. Cecchin F., Atallah J., Walsh E.P., Triedman J.K., Alexander M.E., Berul C.I. Lead extraction in pediatric and congenital heart disease patients. Circ. Arrhythm. Electrophysiol. 2010; 3 (5): 437–44. DOI: 10.1161/CIRCEP.110.957324
  32. Kubus P., Materna O., Gebauer R.A., Matejka T., Gebauer R., Tlaskal T. et al. Permanent epicardial pacing in children: long-term results and factors modifying outcome. Europace. 2012; 14 (4): 509–14. DOI: 10.1161/CIRCEP.110.957324
  33. McCanta A.C., Schaffer M.S., Collins K. Pediatric and Adult Congenital Endocardial Lead Extraction or Abandonment Decision (PACELEAD) survey of lead management. Pacing Clin. Electrophysiol. 2011; 34 (12): 1621–7. DOI: 10.1111/j.1540-8159.2011.03226.x
  34. Hofferberth S.C., Alexander M.E., Mah D.Y., Bautista-Hernandez V., del Nido P.J., Fynn-Thompson F. Impact of pacing on systemic ventricular function in Ltransposition of the great arteries. J. Thorac. Cardiovasc. Surg. 2016; 151 (1): 131–8. DOI: 10.1016/j.jtcvs. 2015.08.064

About Authors

  • Sarmat G. Khasiev, Postgraduate; ORCID
  • Viktor B. Samsonov, Dr. Med. Sc., Leading Researcher;ORCID
  • Viktor S. Mataev, Cand. Med. Sc., Researcher; ORCID

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